Glutaric Aciduria type 1 (GA-1)

Glutaric Aciduria is an inherited metabolic disease that involves the metabolism of three amino acids: lysine, hydroxylisine and tryptophan.

Amino acids are the constituent units of proteins and are therefore daily taken as part of one’s diet. Individuals with Glutaric Aciduria type 1 should be on a lysine-free and low-tryptophan diet.

Given the impossibility of excluding these amino acids from natural proteins, the patient should, in general, follow a protein-free diet, supplemented with adequate protein substitutes (free from lysine and with a low tryptophan content). The treatment is, however, customized according to the needs of the individual patient.

PIAM, always attentive to the problems related to rare or low-prevalence diseases, offers a diversified range of specific protein substitutes for the correct nutritional management of patients suffering from Glutaric Aciduria type 1, providing tailor-made solutions for all ages, from childhood up to adulthood.